PROTEUS-SYNDROME - CLINICAL-FEATURES AND DIFFERENTIAL-DIAGNOSIS

被引:1
|
作者
BAYKAL, C
GOGUS, A
GURSOY, EO
ERGUN, T
DOMANIC, U
机构
[1] ISTANBUL UNIV, FAK MED, ORTHOPAD & TRAUMATOL KLIN, ISTANBUL, TURKEY
[2] UNIV MARMARA, FAK MARMARA, DERMATOL KLIN & MED, MARMARA, GERMANY
来源
HAUTARZT | 1994年 / 45卷 / 04期
关键词
PROTEUS SYNDROME; EPIDERMAL NEVUS; HEMIHYPERTROPHY; EXOSTOSIS; PLANTAR MASSES;
D O I
10.1007/s001050050067
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
A case with various skeletal abnormalities, soft tissue masses and skin lesions diagnosed as Proteus syndrome is reported. Proteus syndrome is included in the differential diagnosis of many disorders, because of the polymorphous nature of its clinical manifestations. It is a rare disorder and leads to functional disabilities as well as cosmetic and psychological problems. Early diagnosis and careful follow-up with appropriate surgical interventions is important in preventing long-term complications.
引用
收藏
页码:237 / 242
页数:6
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