PORTAL-VEIN THROMBOSIS AS A COMPLICATION OF NOCTURNAL PAROXYSMAL HEMOGLOBINURIA

被引:0
|
作者
NICOLAS, JM
CERVANTES, F
LOPEZGUILLERMO, A
QUINTEROS, L
ROZMAN, C
机构
来源
REVISTA CLINICA ESPANOLA | 1990年 / 187卷 / 06期
关键词
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A patient suffering nocturnal paroxysmal hemoglobinuria (HPN) associated with the recovery phase of a severe medullar aplasia, and who presented a thrombosis of the portal vein is described. The sudden appearance of fast growing splenomegaly with signs of hypersplenism was the sign that made us suspect of a portal thrombosis. The diagnosis was confirmed by an ultrasound and an angiographic study with DIVAS. The problems due to the thromboembolic complications of HPN are reviewed and the therapeutic possibilities are discussed.
引用
收藏
页码:287 / 289
页数:3
相关论文
共 50 条
  • [41] ISOLATED PORTAL-VEIN THROMBOSIS - AN EXCEPTIONAL COMPLICATION OF CHRONIC-PANCREATITIS
    BAIL, JP
    ANDIVOT, T
    LEAL, T
    MENUT, P
    NOUSBAUM, JB
    CHARLES, JF
    [J]. ANNALES DE CHIRURGIE, 1993, 47 (01): : 47 - 51
  • [42] TREATMENT WITH STREPTOKINASE FOR HEPATIC VEIN-THROMBOSIS (HVT) IN PAROXYSMAL NOCTURNAL HEMOGLOBINURIA (PNH)
    WEST, T
    MURPHY, P
    CROOK, L
    ODELL, R
    EURENIUS, K
    [J]. CLINICAL RESEARCH, 1978, 26 (01): : A22 - A22
  • [43] Thrombosis in Paroxysmal Nocturnal Hemoglobinuria - insights into the role of complement in thrombosis
    Weitz, Ilene C.
    [J]. THROMBOSIS RESEARCH, 2010, 125 : S106 - S107
  • [44] Postpartum thrombotic complication in a patient with paroxysmal nocturnal hemoglobinuria
    Gessoni, Gianluca
    Canistro, Rosa
    Bergamini, Luca
    Valverde, Sara
    Gessoni, Francesca
    Nani, Giovanna
    Beggio, Samanta
    Spillare, Pietro
    Tregnaghi, Alberto
    [J]. BLOOD COAGULATION & FIBRINOLYSIS, 2015, 26 (04) : 458 - 463
  • [45] CEREBRAL VENOUS THROMBOSIS IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
    ALFARO, A
    [J]. JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY, 1992, 55 (05): : 412 - 412
  • [46] CEREBRAL VENOUS THROMBOSIS IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
    VANVLEYMEN, B
    DEHAENE, I
    VANHOOF, A
    PATTYN, G
    [J]. ACTA NEUROLOGICA BELGICA, 1987, 87 (02) : 80 - 87
  • [47] Prediction of thrombosis risk in patients with paroxysmal nocturnal hemoglobinuria
    Huang, Yuzhou
    Liu, Xinjian
    Chen, Fangfei
    Zhou, Wenzhe
    Li, Hongmin
    Long, Zhangbiao
    Yang, Chen
    Chen, Miao
    Han, Bing
    [J]. ANNALS OF HEMATOLOGY, 2019, 98 (10) : 2283 - 2291
  • [48] MICROVASCULAR THROMBOSIS OF THE BOWEL IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
    WILLIAMSON, LM
    JOHNSTONE, JM
    PRESTON, FE
    [J]. JOURNAL OF CLINICAL PATHOLOGY, 1987, 40 (08) : 930 - 931
  • [49] DOUBLE PORTAL AND HEPATIC VENOUS THROMBOSIS REVEALING A PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA AND REGRESSIVE WITH HEPARIN
    SCHMETS, L
    HAGEGE, H
    MERLET, C
    ZYLBERBERG, H
    CHOUSTERMAN, M
    [J]. GASTROENTEROLOGIE CLINIQUE ET BIOLOGIQUE, 1993, 17 (12): : 955 - 958
  • [50] DURAL SINUS THROMBOSIS IN PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA
    DONHOWE, SP
    LAZARO, RP
    [J]. CLINICAL NEUROLOGY AND NEUROSURGERY, 1984, 86 (03) : 149 - 152