N-ACETYLNEURAMINIC ACID ACCUMULATION IN A BUOYANT LYSOSOMAL FRACTION OF CULTURED FIBROBLASTS FROM PATIENTS WITH INFANTILE GENERALIZED N-ACETYLNEURAMINIC ACID STORAGE DISEASE

被引:16
|
作者
HILDRETH, J
SACKS, L
HANCOCK, LW
机构
[1] UNIV CHICAGO,JOSEPH P KENNEDY JR MENTAL RETARDAT RES CTR,DEPT MOLEC BIOL,CHICAGO,IL 60637
[2] UNIV CHICAGO,JOSEPH P KENNEDY JR MENTAL RETARDAT RES CTR,DEPT BIOCHEM,CHICAGO,IL 60637
关键词
D O I
10.1016/S0006-291X(86)80066-3
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:838 / 844
页数:7
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