EARLY DIAGNOSIS OF MULTIPLE HAMARTOMA AND NEOPLASIA SYNDROME (COWDEN DISEASE) - THE ROLE OF THE DENTIST

被引:17
|
作者
MIGNOGNA, MD
LOMUZIO, L
RUOCCO, V
BUCCI, E
机构
[1] UNIV NAPLES ATENO II, FAC MED, SCH MED, INST DERMATOL, NAPLES, ITALY
[2] UNIV NAPLES FEDERICO II, FAC MED, SCH DENT, DEPT ORAL PATHOL, NAPLES, ITALY
关键词
D O I
10.1016/S1079-2104(05)80222-7
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
A typical case of Cowden disease is presented. This is a rare mucocutaneous disease, genetically determined, with multiple organ system involvement in which a malignancy, particularly of breast and thyroid gland, may develop. The disease can be diagnosed in its early stages by gingival and cutaneous manifestations. We emphasize that the dentist may be the first health care professional who recognizes the syndrome, which is a crucial step to prevent and cure the predictable malignancy.
引用
收藏
页码:295 / 299
页数:5
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