XANTHOGRANULOMATOUS PYELONEPHRITIS AND SYSTEMIC AMYLOIDOSIS - REPORT OF 2 NEW CASES AND THE NATURAL-HISTORY OF THIS ASSOCIATION

被引:17
|
作者
LAUZURICA, R
FELIP, A
SERRA, A
SALADIE, JM
MONTSERRAT, E
ENCABO, B
CARALPS, A
机构
[1] HOSP BADALONA GERMANS TRIAS & PUJOL,DEPT UROL,BADALONA,SPAIN
[2] HOSP BADALONA GERMANS TRIAS & PUJOL,DEPT RADIOL,BADALONA,SPAIN
[3] HOSP BADALONA GERMANS TRIAS & PUJOL,DEPT PATHOL,BADALONA,SPAIN
来源
JOURNAL OF UROLOGY | 1991年 / 146卷 / 06期
关键词
KIDNEY DISEASES; AMYLOIDOSIS; PYELONEPHRITIS; XANTHOGRANULOMATOUS; NEPHROTIC SYNDROME;
D O I
10.1016/S0022-5347(17)38181-8
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
The association of xanthogranulomatous pyelonephritis and systemic amyloidosis is extremely rare. To our knowledge, despite innumerable cases of xanthogranulomatous pyelonephritis reported in the literature, this association has been described on only 2 occasions. Clinical, analytical and radiographic findings can be highly suggestive of the diagnosis. We report on 2 patients with xanthogranulomatous pyelonephritis, systemic amyloidosis and the nephrotic: 1 died 4 1/2 years after diagnosis and 1 was stable with good general health 3 years after diagnosis. The clinical aspects as well as the treatment given to both patients are discussed. We describe the natural history of an association that due to its rarity is not currently well known.
引用
收藏
页码:1603 / 1606
页数:4
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