LYSOSOMAL ENZYME VARIATIONS IN CULTURED NORMAL SKIN FIBROBLASTS

被引:52
|
作者
MILUNSKY, A
SPIELVOGEL, C
KANFER, JN
机构
关键词
D O I
10.1016/0024-3205(72)90219-6
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1101 / +
页数:1
相关论文
共 50 条
  • [31] IMPLANTS OF GENETICALLY-MODIFIED SKIN FIBROBLASTS FOR LYSOSOMAL-ENZYME DELIVERY - STUDIES IN NEWBORN MUTANT MICE AND IN NORMAL DOGS
    MOULLIER, P
    BOHL, D
    CARDOSO, J
    HEARD, JM
    DANOS, O
    JOURNAL OF CELLULAR BIOCHEMISTRY, 1994, : 239 - 239
  • [32] [C-14] METHYLAMINE ACCUMULATION IN CULTURED HUMAN SKIN FIBROBLASTS - A BIOCHEMICAL TEST FOR LYSOSOMAL STORAGE AND LYSOSOMAL DISEASES
    KOPITZ, J
    GERHARD, C
    HOFLER, P
    CANTZ, M
    CLINICA CHIMICA ACTA, 1994, 227 (1-2) : 121 - 133
  • [33] COLLAGEN-SYNTHESIS IN CULTURED NORMAL HUMAN-SKIN FIBROBLASTS
    KELLEY, LA
    IN VITRO-JOURNAL OF THE TISSUE CULTURE ASSOCIATION, 1980, 16 (03): : 218 - 218
  • [34] CU-64 METABOLISM IN MENKES AND NORMAL CULTURED SKIN FIBROBLASTS
    BERATIS, NG
    PRICE, P
    LABADIE, G
    HIRSCHHORN, K
    PEDIATRIC RESEARCH, 1978, 12 (06) : 699 - 702
  • [35] THE CHARACTERIZATION OF NORMAL AND SCLERODERMA SKIN FIBROBLASTS CULTURED IN A COLLAGEN GEL MATRIX
    MAYES, MD
    WALKER, ER
    FREDERICKSON, RG
    PRINCE, RK
    DIBARTOLOMEO, AG
    JOURNAL OF RHEUMATOLOGY, 1988, 15 (02) : 268 - 275
  • [36] DIRECT DEMONSTRATION OF BINDING OF A LYSOSOMAL ENZYME, ALPHA-L-IDURONIDASE, TO RECEPTORS ON CULTURED FIBROBLASTS
    ROME, LH
    WEISSMANN, B
    NEUFELD, EF
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1979, 76 (05) : 2331 - 2334
  • [37] BIOCHEMICAL-MECHANISMS OF AMINOGLYCOSIDE CELL TOXICITY .1. THE UPTAKE OF GENTAMICIN BY CULTURED SKIN FIBROBLASTS AND THE ALTERATION OF LYSOSOMAL-ENZYME ACTIVITIES
    OSHIMA, M
    HASHIGUCHI, M
    SHINDO, N
    SHIBATA, S
    JOURNAL OF BIOCHEMISTRY, 1986, 100 (06): : 1575 - 1582
  • [38] PHOTOLYSIS OF THE LYSOSOMAL NEURAMINIDASE IN CULTURED HUMAN-SKIN FIBROBLASTS IN THE PRESENCE OF A PHOTOREACTIVE COMPETITIVE INHIBITOR
    WARNER, TG
    LOFTIN, SK
    ENZYME, 1989, 42 (02) : 103 - 109
  • [39] TRANSPORT AND PROCESSING OF ENDOCYTOSED LYSOSOMAL ALPHA-GLUCOSIDASE IN CULTURED HUMAN-SKIN FIBROBLASTS
    ELFERINK, RPJO
    VANDOORNVANWAKEREN, J
    HENDRIKS, T
    STRIJLAND, A
    TAGER, JM
    EUROPEAN JOURNAL OF BIOCHEMISTRY, 1986, 158 (02): : 339 - 344
  • [40] METACHROMASIA AND ASSAY FOR LYSOSOMAL ENZYMES IN SKIN FIBROBLASTS CULTURED FROM PATIENTS WITH CYSTIC FIBROSIS AND CONTROLS
    KRAUS, I
    ANTONOWICZ, I
    SHAH, H
    LAZARUS, H
    SHWACHMAN, H
    PEDIATRICS, 1971, 47 (06) : 1010 - +