HALLERVORDEN-SPATZ DISEASE - RESULTS OF COMPUTED-TOMOGRAPHY AND MAGNETIC-RESONANCE-IMAGING ARE HIGHLY SUSPECT FOR THIS DIAGNOSIS INTRA VITAM

被引:0
|
作者
KURLEMANN, G
BONGARTZ, G
KUCHELMEISTER, K
PALM, DG
机构
关键词
HALLERVORDEN-SPATZ; COMPUTED TOMOGRAPHY; MAGNETIC RESONANCE IMAGING; GLOBUS PALLIDUS;
D O I
暂无
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
We report the case of a female patient with a progressive therapy-resistant extrapyramidal movement disorder. Cranial computed tomography showed symetrical hyperdensities in the globus pallidus. The same areas are of decreased signal intensity in magnetic resonance imaging. These findings suggest an increased iron accumulation. The clinical symptoms and the radiological findings of the cerebrum are highly indicative for a Hallervorden-Spatz disease.
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页码:626 / 628
页数:3
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