GLUCOSE-CONTAINING OLIGOSACCHARIDES IN URINE OF PATIENTS WITH GLYCOGEN-STORAGE DISEASE TYPE-II AND TYPE-III

被引:26
|
作者
LENNARTSON, G [1 ]
LUNDBLAD, A [1 ]
LUNDSTEN, J [1 ]
SVENSSON, S [1 ]
HAGER, A [1 ]
机构
[1] UNIV HOSP LINKOPING,DEPT PAEDIAT,S-58185 LINKOPING,SWEDEN
来源
EUROPEAN JOURNAL OF BIOCHEMISTRY | 1978年 / 83卷 / 02期
关键词
D O I
10.1111/j.1432-1033.1978.tb12098.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:325 / 334
页数:10
相关论文
共 50 条
  • [21] USE OF LEUKOCYTES AS AN AID IN DIAGNOSIS OF GLYCOGEN-STORAGE DISEASE TYPE-II (POMPES DISEASE)
    KOSTER, JF
    SLEE, RG
    HULSMANN, WC
    EUROPEAN JOURNAL OF CLINICAL INVESTIGATION, 1974, 4 (05) : 331 - 331
  • [22] COMPARATIVE PATHOLOGY OF THE CANINE MODEL OF GLYCOGEN-STORAGE DISEASE TYPE-II (POMPES DISEASE)
    WALVOORT, HC
    DORMANS, JAMA
    VANDENINGH, TSGAM
    JOURNAL OF INHERITED METABOLIC DISEASE, 1985, 8 (01) : 38 - 46
  • [23] USE OF LEUKOCYTES AS AN AID IN DIAGNOSIS OF GLYCOGEN-STORAGE DISEASE TYPE-II (POMPES DISEASE)
    KOSTER, JF
    SLEE, RG
    HULSMANN, WC
    CLINICA CHIMICA ACTA, 1974, 51 (03) : 319 - 325
  • [24] INCORPORATION OF [C-14] GLUCOSE INTO ALPHA-1,4 BONDS OF GLYCOGEN BY LEUKOCYTES AND FIBROBLASTS OF PATIENTS WITH TYPE-III GLYCOGEN-STORAGE DISEASE
    GUTMAN, A
    BARASH, V
    SCHRAMM, H
    DECKELBAUM, RJ
    GRANOT, E
    AKER, M
    KOHN, G
    PEDIATRIC RESEARCH, 1985, 19 (01) : 28 - 32
  • [25] 1ST TRIMESTER PRENATAL-DIAGNOSIS OF GLYCOGEN-STORAGE DISEASE TYPE-III
    MAIRE, I
    MANDON, G
    MATHIEU, M
    JOURNAL OF INHERITED METABOLIC DISEASE, 1989, 12 : 292 - 294
  • [26] ULTRASTRUCTURE OF MYOCARDIUM IN GLYCOGEN-STORAGE DISEASE, TYPE-II - ANATOMOCLINICAL CASE-REPORT
    BOUHOUR, JB
    LEFEVRE, M
    DELAJARTRE, AY
    PETITIER, H
    COEUR, 1977, 8 (05): : 1021 - 1030
  • [27] NIGHTLY INTERMITTENT POSITIVE PRESSURE VENTILATION IN A CASE OF TYPE-II GLYCOGEN-STORAGE DISEASE
    BUDDESTEFFEN, C
    GRAVINGHOFF, L
    ALBANI, M
    HELLWEGE, HH
    KOHLSCHUTTER, A
    DEUTSCHE MEDIZINISCHE WOCHENSCHRIFT, 1989, 114 (28-29) : 1114 - 1116
  • [28] CARDIOMYOPATHY OF GLYCOGEN-STORAGE-DISEASE TYPE-III
    CARVALHO, JS
    MATTHEWS, EE
    LEONARD, JV
    DEANFIELD, J
    HEART AND VESSELS, 1993, 8 (03) : 155 - 159
  • [29] GENETIC STUDIES IN GLYCOGEN STORAGE DISEASE TYPE-III
    WAALER, PE
    GARATUNT.O
    MOE, PJ
    ACTA PAEDIATRICA SCANDINAVICA, 1970, 59 (05): : 529 - &
  • [30] Obstructive hypertrophic cardiomyopathy in type III glycogen-storage disease
    Cuspidi, C
    Sampieri, L
    Pelizzoli, S
    Pontiggia, G
    Zanchetti, A
    Nappo, A
    Caputo, V
    Matturri, L
    ACTA CARDIOLOGICA, 1997, 52 (02) : 117 - 123