PEUTZ JEGHERS SYNDROME PRESENTING WITH ACUTE INTESTINAL OBSTRUCTION: A RARE CASE REPORT WITH REVIEW OF LITERATURES

被引:0
|
作者
Hota, P. K. [1 ]
Reddy, G. Narasimha [1 ]
Rajasekhar, G. [1 ]
Mohan, C. Nalini [2 ]
机构
[1] Mamata Med Coll, Dept Gen Surg, Surg, Khammam 507002, Telangana, India
[2] Mamata Med Coll, Dept Pathol, Khammam 507002, Telangana, India
关键词
Peutz-Jeghers syndrome; intussusception; acute intestinal obstruction;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Background: Peutz-Jeghers syndrome is a rare genetic disorder presenting in young age with mucocutaneous pigmentation and hamartomatous polyposis. Method: We report a case of Peutz-Jeghers syndrome in a 16 year old boy presenting with acute intestinal obstruction. Results: Imaging studies revealed intussusception. He had mucocutaneous pigmentation and multiple hamartomatous polyps which were diagnosed histologically. The unusual presentation of the case and its successful management has prompted us to report the case with literature review.
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页码:98 / 101
页数:4
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