Tuberous sclerosis complex: A case report

被引:8
|
作者
Sarkar, Soumyabrata [1 ]
Khaitan, Tanya [1 ]
Sinha, Rupam [1 ]
Kabiraj, Arpita [2 ]
机构
[1] Haldia Inst Dent Sci & Res, Dept Oral Med & Radiol, Haldia 721645, W Bengal, India
[2] Haldia Inst Dent Sci & Res, Dept Oral Pathol & Microbiol, Haldia 721645, W Bengal, India
关键词
Fibromas; hamartomas; subependymal nodules;
D O I
10.4103/0976-237X.183071
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
Tuberous sclerosis complex is an unusual autosomal dominant neurocutaneous syndrome characterized by the development of benign tumors affecting different body systems affecting the brain, skin, retina, and viscera. It is characterized by cutaneous changes, neurologic conditions, and the formation of hamartomas in multiple organs leading to morbidity and mortality. The most common oral manifestations are fibromas, gingival hyperplasia, and enamel hypoplasia. The management of these patients is often multidisciplinary involving specialists from various fields. Here, we present a case report of a 26-old-year male patient with characteristic clinical, radiological, and histological features of tuberous sclerosis complex.
引用
收藏
页码:236 / 239
页数:4
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