CONGENITAL LOBAR EMPHYSEMA, A HISTOPATHOLOGICAL STUDY

被引:1
|
作者
Krishna, Radhika O. H. [9 ,1 ]
Geetha, K. [1 ]
Mandakini, T. K. [2 ]
Ameena, Sharf [1 ]
Reddy, Ramesh K. [2 ]
Rao, Bhuvaneshwar N. [2 ]
Reddy, Srinivas P. [2 ]
Malleboyina, Ramani [1 ]
机构
[1] Niloufer Hosp, Dept Pathol, Hyderabad, Telangana, India
[2] Niloufer Hosp, Dept Paediat Surg, Hyderabad, Telangana, India
关键词
CLE; Histopathology; Bronchial Cartilage; RAC;
D O I
10.14260/jemds/2015/2432
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Congenital lobar emphysema is a very rare congenital cystic malformation of the lung that can cause acute respiratory distress early in life. This study reviews 19 cases of CLE over a period of 5 years at a Tertiary Pediatric Referral Center. The cases were studied with special emphasis on Histopathological findings of the lobectomy specimens, particularly bronchial cartilage abnormalties, radial alveolar count and their predictive value in pathogenesis of CLE. This condition can mimick other causes of respiratory distress in the neonatal period. Early diagnosis and effective surgical management is curatve.
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页码:16414 / 16416
页数:3
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