Congenital Cystic Adenomatoid Malformation of the Entire Lung

Cogential cystic adenomatoid malformation (CCAM) is a hamartomatous lesion of the lung. During the first 6-8 weeks of pregnancy, distal alveolar tissue enlarges due to the lack of maturation in proximal airways. Final diagnosis of the disease is generally made after the surgical resection of the cyst and histopathological evaluation. Surgical techniques may vary from segmentectomies to pneumonectomies depending on the size of the cyst. The chances of obtaining positive prognosis are quite high in young adults, children, and in patients who are treated by pulmonary resection. A six-year old male patient was presented with a recurrent history of lung infection since he was born. As a result of physical and radiological examinations, it was determined that his left lung was deteriorated. Hence, left pneumonectomy was performed. Postoperative histopathology showed an overlap with CCAM. As CCAM is known to be a rare occurrence for an entire lung, information related to the patient literature was discussed.