FAMILIAL MEDITERRANEAN FEVER AND PERIARTERITIS-NODOSA IN THE SAME PATIENT - A COINCIDENCE

被引:0
|
作者
PECHERE, M
HELFER, C
LAURENCET, FL
机构
[1] SERV URGENCE AMG,GENEVA,SWITZERLAND
[2] HOP MONTHEY,SERV MED,MONTHEY,SWITZERLAND
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中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Familial Mediterranean fever (FMF) chiefly affects patients of Arabic, Jewish, Armenian or Turkish origin and takes the form of recurrent episodes of peritonitis, arthritis or pleurisy. Periarteritis nodosa (PAN) is a vasculitis affecting elderly people and manifested by a general deterioration, unexplained fever and peripheral neuropathy or muscular weakness. We describe a patient presenting both diseases. Ours is the seventh reported case associating these two affections. This association was suspected by SACHS and co-workers who discovered an increased frequency of PAN in patients with FMF compared to the expected rate for the whole population (7). These observations warrant a search for PAN in young patients affected by FMF and showing signs of vasculitis.
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页码:1166 / 1168
页数:3
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