A CASE OF NEUROFIBROMATOSIS-2 PRESENTING WITH A MONONEURITIS MULTIPLEX

被引:17
|
作者
KILPATRICK, TJ
HJORTH, RJ
GONZALES, MF
机构
[1] AUSTRALIA DEPT NEUROL, PARKVILLE, VIC 3050, AUSTRALIA
[2] DEPT ANAT PATHOL, NEUROPATHOL LAB, PARKVILLE, VIC 3050, AUSTRALIA
来源
关键词
D O I
10.1136/jnnp.55.5.391
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A patient with neurofibromatosis 2 had an asymmetrical peripheral neuropathy. A nerve biopsy specimen revealed neurofibromatous changes, and the neuropathy may have been a direct consequence of neurofibromatosis. An apparent clinical response to immunosuppressive treatment and plasma exchange is also reported.
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页码:391 / 393
页数:3
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