EPIDERMOLYSIS-BULLOSA

被引:21
|
作者
LIN, AN
CARTER, DM
机构
来源
ANNUAL REVIEW OF MEDICINE | 1993年 / 44卷
关键词
BLISTERING DISEASE;
D O I
10.1146/annurev.med.44.1.189
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
Epidermolysis bullosa is a group of genetically determined diseases characterized by abnormal fragility of the skin and mucosa. In this chapter, we review current thinking about classification, pathogenesis, and molecular genetics, and we discuss management guidelines.
引用
收藏
页码:189 / 199
页数:11
相关论文
共 50 条
  • [1] EPIDERMOLYSIS-BULLOSA
    KERO, M
    NIEMI, KM
    [J]. INTERNATIONAL JOURNAL OF DERMATOLOGY, 1986, 25 (02) : 75 - 82
  • [2] EPIDERMOLYSIS-BULLOSA
    EZQUERROESCRIBANO, T
    FERNANDEZLATORRE, F
    PUEYOLANDA, I
    GUZMANFERNANDEZ, A
    FERNANDEZBLANCO, JRJ
    [J]. RADIOLOGIA, 1979, 21 (05): : 377 - 378
  • [3] EPIDERMOLYSIS-BULLOSA
    LEIDER, M
    BAER, RL
    [J]. ARCHIVES OF DERMATOLOGY AND SYPHILOLOGY, 1945, 51 (06): : 409 - 409
  • [4] EPIDERMOLYSIS-BULLOSA
    ANDREWS, GC
    [J]. ARCHIVES OF DERMATOLOGY AND SYPHILOLOGY, 1946, 54 (02): : 254 - 254
  • [5] EPIDERMOLYSIS-BULLOSA PRURIGINOSA - DYSTROPHIC EPIDERMOLYSIS-BULLOSA WITH DISTINCTIVE CLINICOPATHOLOGICAL FEATURES
    MCGRATH, JA
    SCHOFIELD, OMV
    EADY, RAJ
    [J]. BRITISH JOURNAL OF DERMATOLOGY, 1994, 130 (05) : 617 - 625
  • [6] PRETIBIAL EPIDERMOLYSIS-BULLOSA
    GASSIA, V
    BAZEX, J
    ORTONNE, JP
    [J]. JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY, 1991, 24 (04) : 663 - 664
  • [7] JUNCTIONAL EPIDERMOLYSIS-BULLOSA
    CUNLIFFE, WJ
    NORRIS, JFB
    [J]. BRITISH JOURNAL OF DERMATOLOGY, 1987, 117 : 67 - 68
  • [8] ACQUIRED EPIDERMOLYSIS-BULLOSA
    SARRET, Y
    [J]. ANNALES DE DERMATOLOGIE ET DE VENEREOLOGIE, 1990, 117 (09): : 623 - 629
  • [9] EPIDERMOLYSIS-BULLOSA PROGRESSIVA
    HABER, RM
    HANNA, W
    [J]. JOURNAL OF THE AMERICAN ACADEMY OF DERMATOLOGY, 1987, 16 (01) : 195 - 200
  • [10] HEREDITARY EPIDERMOLYSIS-BULLOSA
    WRIGHT, JT
    FINE, JD
    [J]. SEMINARS IN DERMATOLOGY, 1994, 13 (02): : 102 - 107