Familial non-immune hydrops fetalis and congenital pulmonary lymphangiectasia

被引:0
|
作者
P. R. Njølstad
H. Reigstad
J. Westby
A. Espeland
机构
[1] Department of Medical Genetics,
[2] University of Bergen,undefined
[3] N-5021 Bergen,undefined
[4] Norway,undefined
[5] Department of Paediatrics,undefined
[6] University of Bergen,undefined
[7] Haukeland Hospital,undefined
[8] N-5021 Bergen,undefined
[9] Norway E-mail: pal.r.njolstad@bkb.haukeland.no,undefined
[10] Tel.: +47-55-975200,undefined
[11] Fax: +47-55-975147,undefined
[12] Department of Pathology,undefined
[13] University of Bergen,undefined
[14] Bergen,undefined
[15] Norway,undefined
[16] Department of Radiology,undefined
[17] University of Bergen,undefined
[18] Bergen,undefined
[19] Norway,undefined
来源
关键词
Key words Congenital pulmonal lymphangiectasia; Familial; Hydrops fetalis; Lymphoedema;
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学科分类号
摘要
We report on three siblings with non-immune hydrops fetalis. Congenital pulmonary lymphangiectasia was diagnosed in two of them. One of these, a girl still alive and suffering from frequent airway infections, has bilateral pleural effusions and distal congenital lymphoedema.
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页码:498 / 501
页数:3
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