Conjoined legs: Sirenomelia or caudal regression syndrome?

被引:0
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作者
Sakti Prasad Das
Niranjan Ojha
G. Shankar Ganesh
Ram Narayan Mohanty
机构
[1] SVNIRTAR,Department of Physiotherapy
[2] SVNIRTAR,Department of Prosthetic and Orthotics
[3] SVNIRTAR,Department of Physical Medicine and Rehabilitation
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关键词
Caudal regression syndrome; ectromelia; sirenomelia; conjoined legs;
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摘要
Presence of single umbilical persistent vitelline artery distinguishes sirenomelia from caudal regression syndrome. We report a case of a12-year-old boy who had bilateral umbilical arteries presented with fusion of both legs in the lower one third of leg. Both feet were rudimentary. The right foot had a valgus rocker-bottom deformity. All toes were present but rudimentary. The left foot showed absence of all toes. Physical examination showed left tibia vara. The chest evaluation in sitting revealed pigeon chest and elevated right shoulder. Posterior examination of the trunk showed thoracic scoliosis with convexity to right. The patient was operated and at 1 year followup the boy had two separate legs with a good aesthetic and functional results.
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页码:413 / 416
页数:3
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