Hepatic involvement in hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber disease)

被引：0

作者：

Adam A. Hatzidakis

Christos Gogas

Nickolas Papanikolaou

Dimitrios Samonakis

Diamantis Kofteridis

Nicholas C. Gourtsoyiannis

机构：

[1] Department of Radiology,

[2] University Hospital of Heraklion,undefined

[3] Medical School of Crete,undefined

[4] 71500 Heraklion-Stavrakia,undefined

[5] Crete,undefined

[6] Greece,undefined

[7] Department of Gastroenterology,undefined

[8] University Hospital of Heraklion,undefined

[9] Medical School of Crete,undefined

[10] 71500 Heraklion-Stavrakia,undefined

[11] Crete,undefined

[12] Greece,undefined

[13] Department of Internal Medicine,undefined

[14] University Hospital of Heraklion,undefined

[15] Medical School of Crete,undefined

[16] 71500 Heraklion-Stavrakia,undefined

[17] Crete,undefined

[18] Greece,undefined

来源：

European Radiology | 2002年 / 12卷

关键词：

Rendu-Osler-Weber disease Hepatic vascular malformations Biliary dilatation;

D O I：

暂无

中图分类号：

学科分类号：

摘要：

Hepatic involvement in hereditary hemorrhagic telangiectasia is infrequent and poorly studied. We describe a 62-year-old woman with Rendu-Osler-Weber (ROW) disease and recurrent gastrointestinal bleeding episodes. Blood chemistry was consistent with the presence of cholestasis. Imaging studies revealed prominent vascular abnormalities in the liver and focal intrahepatic bile duct dilatations. The intimate anatomic relationship of the vascular abnormalities to the dilated bile ducts suggests that external vascular compression could have caused their dilatation. To our knowledge, this mechanism has not been proposed in the literature as a possible explanation of biliary dilatation in patients with ROW.

引用

页码：S51 / S55

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