Correction of bone marrow failure in dyskeratosis congenita by bone marrow transplantation

被引：0
|
作者：
A Ghavamzadeh
K Alimoghadam
P Nasseri
M Jahani
A Khodabandeh
G Ghahremani
机构：
[1] Hematology and Bone Marrow Transplantation Unit,Department of Oncology
[2] Shariati Hospital,undefined
[3] Tehran University of Medical Science,undefined
来源：
Bone Marrow Transplantation | 1999年 / 23卷
关键词：
allogeneic bone marrow transplantation; constitutional anemia; dyskeratosis congenita;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
Dyskeratosis congenita is recognized by its dermal lesions and constitutional aplastic anemia in some cases. We report successful allogeneic bone marrow transplantation in two siblings with this disease from their sister, and their long term follow-up. We used reduced doses of cyclophosphamide and busulfan for conditioning instead of total body irradiation. Also, we report late adverse effects of transplantation which are not distinguishable from the natural course of disease.
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页码：299 / 301
页数：2
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