Cardiac Surgery for Kartagener Syndrome

被引:0
|
作者
T. Tkebuchava
L. K. von Segesser
U. Niederhäuser
U. Bauersfeld
M. Turina
机构
[1] Clinic for Cardiovascular Surgery,
[2] University Hospital,undefined
[3] Rämistrasse 100,undefined
[4] Zurich CH-8091,undefined
[5] Switzerland,undefined
[6] Department of Pediatric Cardiology,undefined
[7] Children’s Hospital,undefined
[8] Zurich,undefined
[9] Switzerland,undefined
来源
Pediatric Cardiology | 1997年 / 18卷
关键词
Key words: Kartagener syndrome — Cardiac surgery — Congenital malformation;
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学科分类号
摘要
Two patients (one girl, one boy) with Kartagener syndrome (situs inversus, bronchiectasis, sinusitis), despite pulmonary problems and associated congenital cardiac anomalies, were operated on at the ages of 4 years and 7 years, respectively. They had had previous palliative treatment at the age of 3 months and 1.3 years, respectively. Both postoperative periods after total correction were without significant complications. Long-term follow-up was available for 9 and 19 years, respectively, with no manifestations of heart insufficiency. Both patients are physically active, and neither requires cardiac medication. Patients with Kartagener syndrome and associated congenital cardiac anomalies can successfully undergo multiple cardiac operations with good long-term outcome.
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页码:72 / 73
页数:1
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