A CASE OF HEMOLYTIC-UREMIC SYNDROME WITH THE DEVELOPMENT OF CATASTROPHIC ANTIPHOSPHOLIPID SYNDROME: DIAGNOSIS AND CLINICAL TACTICS

被引:0
|
作者
Dzhumabayeva, B. T. [1 ]
Bityukova, L. S. [1 ]
Tsvetayeva, N. V. [1 ]
Sukhanova, G. A. [1 ]
Vasilyev, S. A. [1 ]
Shavlokhov, V. S. [1 ]
Karagyulyan, S. R. [1 ]
Kaplanskaya, I. B. [1 ]
Petrova, V. I. [1 ]
Avdonin, P. V. [2 ]
机构
[1] Russian Acad Med Sci, Hematol Res Ctr, Moscow 109801, Russia
[2] Russian Acad Sci, NK Koltsov Lab Gen Physiol, Moscow 117901, Russia
来源
TERAPEVTICHESKII ARKHIV | 2010年 / 82卷 / 03期
关键词
hemolytic-uremic syndrome; antiphospholipid syndrome; catastrophic antiphospholipid syndrome; acute renal failure; thrombotic thrombocytopenic purpura; antiphospholipid antibodies; IN-VITRO; ANTIBODIES; PATHOGENESIS; TOXIN; CELLS;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
The paper describes a case of practically simultaneous development of the hemolytic-uremic syndrome (H US) and the catastrophic antiphospholipid syndrome (CAPS) complicated by mesenteric vessel thrombosis and small bowel necrosis. Multimodality treatment comprising volume plasmapheresis, fresh frozen plasma transfusion, hemodialysis, anticoagulant and disaggregant therapy could relieve thrombogenic events, such as pulmonary artery thromboembolism and intestinal necrosis.
引用
收藏
页码:56 / 60
页数:5
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