Vogt-Koyanagi-Harada syndrome is generally a rare multisystemic autoimmune disorder involving with pigmented structures, such as the eye, meninges, inner ear and skin. The syndrome typically presents as an episode of bilateral panuveitis after prodromal symptoms similar to aseptic meningitis. Auditory disturbances include tinnitus, hearing loss and vertigo. We report the case of a 74-year-old woman with blurred vision, two month history of sudden onset hearing loss and tinnitus in the right ear.