Fuchs' Syndrome (Stevens-Johnson Syndrome Without Skin Involvement) in an Adult Male - A Case Report and General Characteristics of the Sporadically Diagnosed Disease

被引:0
|
作者
Sternbersky, Jan
Tichy, Martin [1 ]
机构
[1] Palacky Univ, Fac Med & Dent, Dept Dermatol & Venereol, Olomouc 77520, Czech Republic
关键词
Fuchs' syndrome; Stevens-Johnson syndrome without skin involvement; Mycoplasma infection;
D O I
暂无
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Fuchs' syndrome (Stevens-Johnson syndrome without skin involvement) is a sporadically diagnosed disease. Most authors consider it to be a pure mucosal variant of Stevens-Johnson syndrome; however, some consider the syndrome a separate entity. The complete absence of cutaneous symptoms may be the reason that not all cases of Fuchs' syndrome are diagnosed and properly classified. The authors describe a case of a 22-year-old patient suffering only from mucosal symptoms, diagnosed as Fuchs' syndrome from the context of the tests performed. A Mycoplasma pneumoniae infection triggered the disease onset. Mycoplasma infection, as a trigger factor of Fuchs' syndrome in adults, has so far been described in only a few isolated cases worldwide.
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页码:284 / 287
页数:4
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