An Unusual Case of Congenitally Unguarded Tricuspid Valve Orifice Associated with Pulmonary Valve Atresia and Intact Ventricular Septum

被引:5
|
作者
Takawira, Farirai F. [1 ]
Mitchell, Belinda J. [2 ]
Du Plessis, Dirk J.
机构
[1] Steve Biko Acad Hosp, Dept Paediat, Dept Paediat Cardiol, ZA-0001 Pretoria, South Africa
[2] Steve Biko Acad Hosp, Dept Cardiothorac Surg, ZA-0001 Pretoria, South Africa
关键词
unguarded; tricuspid valve; pulmonary valve atresia; Ebstein's; cavo-pulmonary; Fontan; MALFORMATION;
D O I
10.1111/j.1540-8175.2009.01057.x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We report on a premature neonate who presented with cyanosis soon after birth. She was found on echocardiography to have an unguarded tricuspid valve orifice associated with pulmonary valve atresia and an intact interventricular septum. Owing to the small-sized pulmonary arteries, she was initially managed conservatively with prostaglandin infusion, and at one year of age underwent a successful bidirectional cavo-pulmonary (Glenn) shunt operation. (Echocardiography 2010; 27: 202-204)
引用
收藏
页码:202 / 204
页数:3
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