Large airway obstruction by a chronic dissecting aortic aneurysm in the Marfan syndrome

被引:2
|
作者
Hargreaves, MR [1 ]
Gilbert, TJ [1 ]
Pillai, R [1 ]
Hart, G [1 ]
机构
[1] JOHN RADCLIFFE HOSP,DEPT CARDIAC,OXFORD OX3 9DU,ENGLAND
关键词
Marfan syndrome; aortic dissection;
D O I
10.1136/pgmj.73.865.726
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We describe a patient with the Marfan syndrome who presented with an acute aortic dissection. She underwent composite graft replacement of the aortic root. She returned two years later with dyspnoea and strider due to tracheal compression by a large chronic dissection of the thoracic aorta. Marfan patients are at risk of chronic dissection involving the remaining distal aorta and require regular noninvasive assessment following surgery.
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页码:726 / 728
页数:3
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