Review of surgical and anesthetic management for esophageal atresia with tracheoesophageal fistula, unilateral pulmonary agenesis and dextrocardia

被引:3
|
作者
Rentea, Rebecca M. [1 ]
Oyetunji, Tolulope A. [1 ]
Erkmann, John [2 ]
Knowlton, Joshua Q. [3 ]
Hendrickson, Richard J. [1 ]
机构
[1] Childrens Mercy Hosp, Dept Surg, 2401 Gillham Rd, Kansas City, MO 64108 USA
[2] Childrens Mercy Hosp, Dept Anesthesiol, Kansas City, MO 64108 USA
[3] Childrens Mercy Hosp, Dept Radiol, Kansas City, MO 64108 USA
关键词
Esophageal atresia (EA); Tracheoesophageal fistula (TEF); Unilateral pulmonary agenesis; Lung agenesis; Dextrocardia; LUNG AGENESIS; MALFORMATIONS; DIAGNOSIS; ANOMALIES; APLASIA;
D O I
10.1007/s00383-017-4090-7
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Association of unilateral severe pulmonary atresia or agenesis and esophageal atresia (EA) with or without tracheoesophageal fistula (TEF) and dextrocardia is a rare and highly lethal combination. We report a case of a full-term female infant who had EA with TEF, right lung agenesis, and dextrocardia. Repair of the fistula took place on day of life 3. We describe anesthetic and surgical concerns of this patient's case which are keys to a good operative outcome as well as follow-up for the patient.
引用
收藏
页码:817 / 821
页数:5
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