Left heart abnormalities in connective tissue disease patients with pre-capillary pulmonary hypertension as well as borderline mean pulmonary arterial pressure
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作者:
Tsuchida, Kosei
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St Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, JapanSt Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, Japan
Tsuchida, Kosei
[1
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Yamada, Hidehiro
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St Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, JapanSt Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, Japan
Yamada, Hidehiro
[1
]
Yamasaki, Yoshioki
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St Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, JapanSt Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, Japan
Yamasaki, Yoshioki
[1
]
Suzuki, Kengo
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St Marianna Univ, Sch Med, Div Cardiol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, JapanSt Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, Japan
Suzuki, Kengo
[2
]
Kongoji, Ken
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St Marianna Univ, Sch Med, Div Cardiol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, JapanSt Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, Japan
Kongoji, Ken
[2
]
Akashi, Yoshihiro
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机构:St Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, Japan
Akashi, Yoshihiro
Ozaki, Shoichi
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St Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, JapanSt Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, Japan
Ozaki, Shoichi
[1
]
机构:
[1] St Marianna Univ, Sch Med, Div Rheumatol & Allergol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, Japan
[2] St Marianna Univ, Sch Med, Div Cardiol, Dept Internal Med,Miyamae Ku, Kawasaki, Kanagawa 2168511, Japan
Objective. To describe co-existence of left heart abnormalities among case series of connective tissue disease (CTD) patients who showed pre-capillary pulmonary hypertension (PH) as well as borderline mean pulmonary arterial pressure (mPAP). Methods. From 2010 through 2012, 49 CTD patients suspected to have PH by exercise Doppler echocardiography underwent right heart catheterization. We retrospectively searched for left heart diseases from the available data on Doppler echocardiography, cardiac magnetic resonance imaging (MRI), scintigraphy, and endomyocardial biopsy. Results. Among 49 patients, 11 and 2 had pre- and post-capillary PH, respectively, and another 10 had borderline mPAP. Six of 11 patients with pre-capillary PH showed low pulmonary vascular resistance (PVR) (<= 240 dynes.sec.cm(-5)) and low diastolic pulmonary gradient (< 7 mmHg). Seven of 10 patients with borderline mPAP had normal PVR (< 160) suggesting the presence of left heart abnormalities. Other abnormal findings included increased left atrial volume index and E/E'on Doppler echocardiography, delayed contrast enhancement by MRI, patchy area of hypoperfusion on thallium scintigraphy, and fibrosis in endomyocardial biopsy. Conclusion. The present case series suggested some contribution of left heart abnormalities to the increase in mPAP among CTD patients with pre-capillary PH as well as borderline mPAP.
机构:
Rambam Med Ctr, Dept Cardiol, POB 9602, IL-31096 Haifa, Israel
Technion Israel Inst Technol, Ruth & Bruce Rappaport Fac Med, Haifa, Israel
Technion Israel Inst Technol, Res Inst, Haifa, IsraelRambam Med Ctr, Dept Cardiol, POB 9602, IL-31096 Haifa, Israel
Aronson, Doron
Hardak, Emilia
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Technion Israel Inst Technol, Ruth & Bruce Rappaport Fac Med, Haifa, Israel
Technion Israel Inst Technol, Res Inst, Haifa, Israel
Rambam Hlth Care Campus, Pulm Div, Haifa, IsraelRambam Med Ctr, Dept Cardiol, POB 9602, IL-31096 Haifa, Israel
Hardak, Emilia
Burger, Andrew J.
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机构:
Univ Cincinnati, Div Cardiovasc Dis, Cincinnati, OH USARambam Med Ctr, Dept Cardiol, POB 9602, IL-31096 Haifa, Israel
机构:
CHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Bravos, Elodie
Cottin, Vincent
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Hosp Civils Lyon, Serv Pneumol, Hop Louis Pradel, Lyon, France
Univ Lyon 1, Univ Lyon, UMR754, INRA, Lyon, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Cottin, Vincent
Dauphin, Claire
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机构:
CHU Clermont Ferrand, Serv Cardiol, Clermont Ferrand, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Dauphin, Claire
Bouvaist, Helene
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机构:
CHU Grenoble Alpes, Serv Cardiol, Grenoble, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Bouvaist, Helene
Traclet, Julie
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Hosp Civils Lyon, Serv Pneumol, Hop Louis Pradel, Lyon, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Traclet, Julie
Tresorier, Romain
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CHU Clermont Ferrand, Serv Cardiol, Clermont Ferrand, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Tresorier, Romain
Margelidon-Cozzolino, Victor
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CHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Univ Jean Monnet, Equipe Dysfonct Vasc & Hemostase, UMR1059, INSERM, St Etienne, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Margelidon-Cozzolino, Victor
Bezzeghoud, Souad
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CHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Bezzeghoud, Souad
Ahmad, Kais
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机构:
Hosp Civils Lyon, Serv Pneumol, Hop Louis Pradel, Lyon, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Ahmad, Kais
Accassat, Sandrine
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机构:
CHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
CHU St Etienne, CIC 1408, INSERM, St Etienne, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Accassat, Sandrine
De Magalhaes, Elodie
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机构:
CHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
CHU St Etienne, CIC 1408, INSERM, St Etienne, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
De Magalhaes, Elodie
Mornex, Jean-Francois
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机构:
Hosp Civils Lyon, Serv Pneumol, Hop Louis Pradel, Lyon, France
Univ Lyon 1, Univ Lyon, UMR754, INRA, Lyon, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Mornex, Jean-Francois
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机构:
Pison, Christophe
Bertoletti, Laurent
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机构:
CHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
CHU St Etienne, CIC 1408, INSERM, St Etienne, FranceCHU St Etienne, Serv Med Vasc & Therapeut, St Etienne, France
Bertoletti, Laurent
JOURNAL OF HEART AND LUNG TRANSPLANTATION,
2019,
38
(07):
: 778
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780