Intrahepatic right-to-left shunting after the Fontan operation

被引:5
|
作者
Giamberti, A
Anderson, RH
de Leval, MR
机构
[1] Great Ormond St Hosp Sick Children, Cardiothorac Unit, London WC1N 3JH, England
[2] UCL, Inst Child Hlth, London, England
关键词
congenital heart defects; isomerism; Fontan operation; cyanosis;
D O I
10.1017/S1047951102000689
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We describe two patients with right isomerism, corrected with a fenestrated Fontan operation, who suffered severe progressive cyanosis. Cardiac catheterisation in both revealed a massive right-to-left shunt from the inferior caval vein, through the liver, to a hepatic vein draining directly to the left side of the intra-atrial baffle. The anomalous vein was successfully ligated in both patients.
引用
收藏
页码:308 / 310
页数:3
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