Pulmonary hypertension in polymyositis-dermatomyositis: clinical and hemodynamic characteristics and response to vasoactive therapy

被引:20
|
作者
Minai, O. A. [1 ]
机构
[1] Cleveland Clin, Dept Pulm Allergy & Crit Care, Cleveland, OH 44195 USA
关键词
connective tissue disease; interstitial lung disease; polymyositis-dermatomyositis; pulmonary hypertension; therapy; SYSTEMIC-SCLEROSIS; DISEASE; MANIFESTATIONS; INVOLVEMENT; PATIENT;
D O I
10.1177/0961203309102822
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
The increased incidence of pulmonary hypertension and its association with decreased survival is well-recognised in patients with systemic sclerosis. This association is not widely appreciated in patients with polymyositis-dermatomyositis. We report clinical and hemodynamic characteristics and response to vasoactive therapy in three patients with polymyositis-dermatomyositis and pulmonary hypertension and discuss them in light of the available literature. Lupus (2009) 18, 1006-1010.
引用
收藏
页码:1006 / 1010
页数:5
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