Brown tumour as a complication of secondary hyperparathyroidism in severe long-lasting vitamin D deficiency rickets

被引:20
|
作者
Bereket, A [1 ]
Casur, Y [1 ]
Firat, P [1 ]
Yordam, N [1 ]
机构
[1] Hacettepe Univ, Ihsan Dogramaci Childrens Hosp, Dept Paediat, Ankara, Turkey
关键词
Brown tumour; rickets; hyperparathyroidism; vitamin D; mandibular tumour;
D O I
10.1007/PL00013807
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Brown tumour is a localised form of fibrous-cystic osteitis associated with primary or secondary hyperparathyroidism. Despite the fact that secondary hyperparathyroidism occurs in vitamin D deficiency rickets, no cases of rickets with brown tumour have so far been described. We present a 2.9-year-old girl who had brown tumour of the mandible due to severe vitamin D deficiency rickets. Treatment with vitamin D-3 corrected the hyperparathyroidism rapidly which was followed by gradual regression in tumour size. Conclusion Brown tumour can develop in severe, long-standing vitamin D deficiency rickets and responds to vitamin D treatment.
引用
收藏
页码:70 / 73
页数:4
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