Peutz-Jeghers syndrome

被引：20
|
作者：
McGarrity, TJ
Kulin, HE
Zaino, RJ
机构：
[1] Penn State Univ, Milton S Hershey Med Ctr, Dept Med, Sect Gastroenterol & Hepatol, Hershey, PA 17033 USA
[2] Penn State Univ, Milton S Hershey Med Ctr, Dept Pediat, Endocrinol Sect, Hershey, PA 17033 USA
[3] Penn State Univ, Milton S Hershey Med Ctr, Dept Pathol, Hershey, PA 17033 USA
来源：
AMERICAN JOURNAL OF GASTROENTEROLOGY | 2000年 / 95卷 / 03期
关键词：
D O I：
暂无
中图分类号：
R57 [消化系及腹部疾病];
学科分类号：
摘要：
Peutz-Jeghers syndrome (PJS) is an unusual polyposis syndrome that has enjoyed a rich and somewhat confusing history. Mucocutaneous pigmentation and diffuse gastrointestinal hamartomas are the hallmark features of this autosomal dominant inherited condition. Peutz-Jeghers syndrome is now also recognized as a cancer predisposition syndrome. in this review, we highlight the historical aspects of PJS polyposis with special emphasis on its extraintestinal manifestations, particularly genital tract tumors. A PJS management scheme for clinicians is included. (Am J Gastroenterol 2000,95:596-604. (C) 2000 by Am. Coll. of Gastroenterology).
引用
收藏
页码：596 / 604
页数：9
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