Aplasia Cutis Congenita Associated with Fetus Papyraceus

被引:11
|
作者
Lia Pieretti, Maria [1 ]
Alcala, Rebeca [2 ]
Boggio, Paula [1 ]
Noguera-Morel, Lucero [2 ]
Librada Porrino, Maria [3 ]
Luna, Paula C. [4 ]
Hernandez-Martin, Angela [2 ]
Schroh, Roberto [5 ]
Larralde, Margarita [1 ,4 ]
Torrelo, Antonio [2 ]
机构
[1] Hosp Ramos Mejia, Pediat Dermatol Sect, Dept Dermatol, Buenos Aires, DF, Argentina
[2] Hosp Nino Jesus, Dept Dermatol, Madrid, Spain
[3] Univ Hosp San Cecilio, Dept Dermatol, Granada, Spain
[4] Hosp Aleman, Dept Dermatol, Buenos Aires, DF, Argentina
[5] Hosp Ramos Mejia, Dept Pathol, Buenos Aires, DF, Argentina
关键词
LIMB DEFECTS; MANAGEMENT; PROPOSAL; TRUNK; TWIN;
D O I
10.1111/pde.12651
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Aplasia cutis congenita (ACC), or congenital absence of skin, is a heterogeneous condition that may be due to varied mechanisms. ACC has rarely been reported in association with fetus papyraceus, representing a peculiar phenotype of ACC. We present six new cases of neonates born with symmetric ACC associated with intrauterine fetal demise of co-twins during the late first or early second trimester.
引用
收藏
页码:858 / 861
页数:4
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