Renal Amyloidosis in Juvenile Rheumatoid Arthritis

被引:0
|
作者
Akhtar, Naureen [1 ,2 ]
Kiran, Sadia [1 ,2 ]
Hussain, Abid [1 ,2 ]
Suleman, Bilquis A. [3 ]
Jaleel, Shahila [3 ]
机构
[1] Childrens Hosp, Dept Pediat Nephrol, Lahore, Pakistan
[2] Inst Child Hlth, Lahore, Pakistan
[3] Sheikh Zayed Hosp, Dept Histopathol, Lahore, Pakistan
关键词
Amyloidosis; Kidneys; Juvenile rheumatoid arthritis; AA-AMYLOIDOSIS;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We report a case of a rare disorder of renal amyloidosis occurring as a complication of juvenile rheumatoid arthritis in a 16-year-old adolescent male. He presented with generalized edema and hypertension. The laboratory work-up showed nephrotic-range proteinuria and hypoalbuminemia and normal renal function despite bilateral shrunken kidneys revealed by the abdominal ultrasound. His renal biopsy showed deposition of amyloid fibrils in the form of homogenous eosinophilic material within the glomeruli demonstrating the pathognomonic apple-green birefringence by polarized light microscopy.
引用
收藏
页码:130 / 132
页数:3
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