Churg-Strauss syndrome (CSS) is a rare necrotizing vasculitis of small- and medium-size blood vessels, characterized by granulomas and hypereosinophilia with organ involvement. Cardiac involvement in these patients is a poor prognostic factor and accounts for 50% of deaths. CSS can affect any layer of the heart, and ischemia secondary to vasculitis and/or eosinophilic infiltration are the two proposed mechanisms for this type of involvement. Several imaging modalities, such as two-dimensional echocardiogram, positron emission tomography and cardiac magnetic resonance, have been used to detect cardiac involvement in CSS patients. Mortality is as high as 50% without immediate therapy, and usual regimens include intravenous steroids and cyclophosphamide. The authors present a case involving a 48-year-old man newly diagnosed with CSS presenting with a left ventricular mass resolved with steroid therapy.
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Humanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, ItalyHumanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, Italy
Cavallero, Erika
Curzi, Mirko
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Humanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, ItalyHumanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, Italy
Curzi, Mirko
Cioccarelli, Sara Anna
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Humanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, ItalyHumanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, Italy
Cioccarelli, Sara Anna
Papalia, Giulio
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Humanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, ItalyHumanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, Italy
Papalia, Giulio
Ornaghi, Diego
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Humanitas Clin & Res Ctr, Heart Surg, Milan, ItalyHumanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, Italy
Ornaghi, Diego
Bragato, Renato Maria
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Humanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, ItalyHumanitas Clin & Res Ctr, Div Echocardiog, Via Manzoni-56, I-20089 Rozzano, MI, Italy
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Tel Aviv Univ, Sackler Sch Med, Assaf Harofeh Med Ctr, Div Pediat, IL-70300 Zerifin, IsraelTel Aviv Univ, Sackler Sch Med, Assaf Harofeh Med Ctr, Div Pediat, IL-70300 Zerifin, Israel
Youngster, Ilan
Eshel, Gideon
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机构:Tel Aviv Univ, Sackler Sch Med, Assaf Harofeh Med Ctr, Div Pediat, IL-70300 Zerifin, Israel
Eshel, Gideon
Abu-Kishak, Ibrahim
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机构:Tel Aviv Univ, Sackler Sch Med, Assaf Harofeh Med Ctr, Div Pediat, IL-70300 Zerifin, Israel
Abu-Kishak, Ibrahim
Heyman, Eli
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机构:Tel Aviv Univ, Sackler Sch Med, Assaf Harofeh Med Ctr, Div Pediat, IL-70300 Zerifin, Israel
Heyman, Eli
Baram, Shaul
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机构:Tel Aviv Univ, Sackler Sch Med, Assaf Harofeh Med Ctr, Div Pediat, IL-70300 Zerifin, Israel