Ivacaftor-treated Patients with Cystic Fibrosis Derive Long-Term Benefit Despite No Short-Term Clinical Improvement

被引：17
|
作者：
Heltshe, Sonya L. [1 ,2 ]
Rowe, Steven M. [3 ]
Skalland, Michelle [2 ]
Baines, Arthur [2 ]
Jain, Manu [4 ]
机构：
[1] Univ Washington, Sch Med, Seattle, WA 98195 USA
[2] CFF Therapeut Dev Network Coordinating Ctr Seattl, Seattle, WA USA
[3] Univ Alabama Birmingham, Birmingham, AL USA
[4] Northwestern Univ, Feinberg Sch Med, Chicago, IL 60611 USA
来源：
AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE | 2018年 / 197卷 / 11期
关键词：
MUTATION; POTENTIATOR; EFFICACY; SAFETY;
D O I：
10.1164/rccm.201710-2046LE
中图分类号：
R4 [临床医学];
学科分类号：
1002 ; 100602 ;
摘要：
引用
收藏
页码：1483 / 1486
页数：4
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