Treatment of haemophilia in Austria

被引:0
|
作者
Pabinger, Ingrid [1 ]
Heistinger, Max [2 ]
Muntean, Wolfgang [3 ]
Reitter-Pfoertner, Sylvia-Elisabeth [1 ]
Rosenlechner, Sabine [4 ]
Schindl, Thomas [5 ]
Schuster, Gerhard [6 ]
Streif, Werner [7 ]
Thom, Katharina [8 ]
Male, Christoph [8 ]
机构
[1] Med Univ Wien, Univ Klin Innere Med 1, Klin Abt Hematol & Hemostaseol, A-1090 Vienna, Austria
[2] LKH Klagenfurt, Med Abt 1, Klagenfurt, Austria
[3] Med Univ Graz, Univ Klin Kinder & Jugendheilkunde, Graz, Austria
[4] Klin Prof Schedel, Kellberg Bei Passau, Germany
[5] Osterreich Hamophilie Gesell, Vienna, Austria
[6] Blutzentrale Roten Kreuzes, Linz, Austria
[7] Med Univ Innsbruck, Dept Kinder & Jugendheilkunde, A-6020 Innsbruck, Austria
[8] Med Univ Wien, Univ Klin Kinder & Jugendheilkunde, Vienna, Austria
关键词
Haemophilia; Guidelines; Clotting factor concentrates; Desmopressin; ACTIVATED FACTOR-VII; HEREDITARY BLEEDING DISORDERS; IMMUNE TOLERANCE THERAPY; RECOMBINANT FACTOR-VIII; PROPHYLACTIC TREATMENT; SECONDARY PROPHYLAXIS; CONGENITAL HEMOPHILIA; ORTHOPEDIC-SURGERY; BRITISH-COMMITTEE; DENTAL EXTRACTION;
D O I
10.1007/s00508-015-0872-x
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
This guideline which is endorsed by the Austrian Society of Haemophilia, the Austrian Society of Paediatrics, and the Austrian Society of Haematology & Medical Oncology is intended to give a clear and practical guidance for diagnosing and treating haemophilia in Austria. In the treatment of haemophilia there are few controlled interventional trials, and recommendations usually have a rather low level of evidence. The main basis for this paper are the new international guidelines by the World Federation of Hemophilia, published in 2013. These were adapted according to the local situation and experience. Covered topics are diagnostics, control visits, pharmacological treatment options, prophylaxis and treatment in children and adults, possible problems arising in haemophilia carriers and special aspects like home therapy, options for venous catheters, management of various traumas, bleedings and interventions, including dental procedures, and last not least inhibitors and their treatment.
引用
收藏
页码:S115 / S130
页数:16
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