Familial hypokalemic periodic paralysis in pregnancy: A case report

被引:5
|
作者
Frappaolo, Anna [1 ]
Vadnais, Mary [1 ]
机构
[1] Atrius Hlth, Maternal Fetal Med, Boston, MA USA
关键词
familial hypokalemic periodic paralysis; muscle weakness; potassium; pregnancy; prenatal care;
D O I
10.1111/jog.14015
中图分类号
R71 [妇产科学];
学科分类号
100211 ;
摘要
Familial hypokalemic periodic paralysis (f-hypoPP) is a rare neuromuscular disorder causing intermittent muscle paralysis. Pregnancy can exacerbate f-hypoPP, yet obstetric management is not well documented. We present a case of a nulliparous woman with f-hypoPP, outlining a complete prenatal care plan generalizable to other women with known f-hypoPP. To our knowledge, this is the first obstetric f-hypoPP case to prioritize intrapartum oral potassium over intravenous potassium, as well as to outline the importance of multidisciplinary care. The patient had a spontaneous vaginal delivery at term with an uneventful postpartum period. Muscle weakness and episodes of relative hypokalemia in the second trimester and during labor were effectively treated with oral potassium supplementation. Care was provided by a multidisciplinary team, and caution was taken to avoid known triggers of paralytic episodes.
引用
收藏
页码:1608 / 1612
页数:5
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