Variegate porphyria

被引:1
|
作者
Sandhu, K [1 ]
Kumar, B [1 ]
机构
[1] Postgrad Inst Med Educ & Res, Dept Dermatol Venerol & Leprol, Chandigarh 160012, India
来源
JOURNAL OF DERMATOLOGY | 2004年 / 31卷 / 05期
关键词
variegate porphyria; porphyria; India;
D O I
10.1111/j.1346-8138.2004.tb00699.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Variegate porphyria is a rare, hereditary form of hepatic porphyria characterized by acute systemic symptoms as in acute intermittent porphyria in addition to cutaneous symptoms simulating porphyria cutanea tarda. We describe a 22-year-old female from India who first presented to the emergency department with acute symptoms and was later confirmed to have variegate porphyria.
引用
收藏
页码:431 / 433
页数:3
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