Primary sclerosing cholangitis: a new cause of distal renal tubular acidosis

被引：4

作者：

Goutaudier, Valentin ^{[1
]}

Szwarc, Ilan ^{[1
]}

Serre, Jean-Emmanuel ^{[1
]}

Pageaux, Georges-Philippe ^{[2
]}

Argiles, Angel ^{[3
,4
]}

Ribstein, Jean ^{[5
]}

机构：

[1] Univ Montpellier, Dept Nephrol Dialysis & Transplantat, Hop Lapeyronie, Sch Med, Montpellier, France

[2] Univ Montpellier, Dept Hepatogastroenterol & Liver Transplantat, Hop St Eloi, Sch Med, Montpellier, France

[3] SAS RD Nephrol, Montpellier, France

[4] Dept Nephrol & Dialysis St Guilhem, Sete, France

[5] Univ Montpellier, Sch Med, Hop Lapeyronie, Dept Hypertens & Internal Med, Montpellier, France

来源：

CLINICAL KIDNEY JOURNAL | 2016年 / 9卷 / 06期

关键词：

distal renal tubular acidosis; liver transplantation; primary sclerosing cholangitis; RARE;

D O I：

10.1093/ckj/sfw085

中图分类号：

R5 [内科学]; R69 [泌尿科学（泌尿生殖系疾病）];

学科分类号：

1002 ; 100201 ;

摘要：

We describe the first case of distal renal tubular acidosis (dRTA) associated with primary sclerosing cholangitis. A 26-year-old Lao-Thai male patient presented with severe jaundice, metabolic acidosis and hypokalaemia. He was diagnosed of dRTA. Liver transplantation resulted in correction of electrolyte disturbances and hyperbilirubinaemia. A fludrocortisone-furosemide test revealed normal urinary acidification, demonstrating no residual dRTA. This observation suggests that dRTA may be an early manifestation of bilirubin-associated nephropathy or the consequence of an immune mechanism.

引用

页码：811 / 813

页数：3

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