α1-antitrypsin deficiency

被引:8
|
作者
Eriksson, S [1 ]
Elzouki, AN [1 ]
机构
[1] Malmo Univ Hosp, Dept Med, S-20502 Malmo, Sweden
来源
BAILLIERES CLINICAL GASTROENTEROLOGY | 1998年 / 12卷 / 02期
关键词
alpha(1)-antitrypsin deficiency; chronic liver disease; emphysema; hepatitis C infection; Pi-type; PiZ; vasculitis;
D O I
10.1016/S0950-3528(98)90134-8
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
alpha(1)-Antitrypsin deficiency (PiZ) is frequent in Caucasian populations. The predominant clinical correlates of this inborn error, i.e. chronic liver disease, emphysema, and vasculitic syndromes including their pathogenetic background are discussed in the present review.
引用
收藏
页码:257 / 273
页数:17
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