We herein report a rare case of microscopic polyangiitis with primary biliary cirrhosis (PBC) and a literature review of six previously reported cases of PBC complicated by anti-neutrophil cytoplasmic antibody-associated vasculitis. Due to the scarcity of similar reports, it was not possible to establish a true overlap syndrome or casual association. When the biliary enzyme levels are elevated in patients with vasculitis, physicians should thus be mindful of the possible coexistence of these diseases.
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Arcispedale Santa Maria Nuova, Dept Rheumatol, Div Med, I-42100 Reggio Emilia, ItalyArcispedale Santa Maria Nuova, Dept Rheumatol, Div Med, I-42100 Reggio Emilia, Italy
Ghinoi, A.
Zuccoli, G.
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Univ Pittsburgh, Dept Radiol, Med Ctr, Pittsburgh, PA 15260 USAArcispedale Santa Maria Nuova, Dept Rheumatol, Div Med, I-42100 Reggio Emilia, Italy
Zuccoli, G.
Pipitone, N.
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Arcispedale Santa Maria Nuova, Dept Rheumatol, Div Med, I-42100 Reggio Emilia, ItalyArcispedale Santa Maria Nuova, Dept Rheumatol, Div Med, I-42100 Reggio Emilia, Italy
Pipitone, N.
Salvarani, C.
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Arcispedale Santa Maria Nuova, Dept Rheumatol, Div Med, I-42100 Reggio Emilia, ItalyArcispedale Santa Maria Nuova, Dept Rheumatol, Div Med, I-42100 Reggio Emilia, Italy