Anti-neutrophil Cytoplasmic Antibody (ANCA)-associated Vasculitis Associated with Primary Biliary Cirrhosis: A Case Report and Literature Review

被引:4
|
作者
Yamashita, Hiroyuki [1 ]
Suzuki, Akitake [1 ]
Takahashi, Yuko [1 ]
Kaneko, Hiroshi [1 ]
Kano, Toshikazu [1 ]
Mimori, Akio [1 ]
机构
[1] Natl Ctr Global Hlth & Med, Div Rheumat Dis, Chiba, Japan
关键词
primary biliary cirrhosis; microscopic polyangiitis; vasculitis; anti-neutrophil cytoplasmic antibodies; PREDNISOLONE TREATMENT; TAKAYASUS-ARTERITIS; CASUAL ASSOCIATION; SJOGRENS-SYNDROME; SINGLE PATIENT; DOUBLE-BLIND; TRIAL; GLOMERULONEPHRITIS; DISEASES; CAUSAL;
D O I
10.2169/internalmedicine.54.3678
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We herein report a rare case of microscopic polyangiitis with primary biliary cirrhosis (PBC) and a literature review of six previously reported cases of PBC complicated by anti-neutrophil cytoplasmic antibody-associated vasculitis. Due to the scarcity of similar reports, it was not possible to establish a true overlap syndrome or casual association. When the biliary enzyme levels are elevated in patients with vasculitis, physicians should thus be mindful of the possible coexistence of these diseases.
引用
收藏
页码:1303 / 1308
页数:6
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