INTERFERENCE WITH POSTTRANSLATIONAL MODIFICATION OF LYSINES MODIFIES STABILITY OF F508DEL CFTR

被引：0
|
作者：
Lee, S. [1 ]
Odeh, H. M. [2 ]
Matunis, M. J. [2 ]
Zeitlin, P. [1 ]
机构：
[1] Johns Hopkins Sch Med, Dept Pediat, Baltimore, MD USA
[2] Johns Hopkins Sch Publ Hlth, Dept Biochem & Mol Biol, Baltimore, MD USA
来源：
PEDIATRIC PULMONOLOGY | 2016年 / 51卷
关键词：
D O I：
暂无
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
68
引用
收藏
页码：218 / 218
页数：1
相关论文
共 50 条
  • [1] Tezacaftor/Ivacaftor in Subjects with Cystic Fibrosis and F508del/F508del-CFTR or F508del/G551D-CFTR
    Donaldson, Scott H.
    Pilewski, Joseph M.
    Griese, Matthias
    Cooke, Jon
    Viswanathan, Lakshmi
    Tullis, Elizabeth
    Davies, Jane C.
    Lekstrom-Himes, Julie A.
    Wang, Linda T.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2018, 197 (02) : 214 - 224
  • [2] COMBINATION OF CORRECTORS AND POTENTIATORS FOR F508DEL CFTR
    Rowe, Steven M.
    Boyle, Michael P.
    PEDIATRIC PULMONOLOGY, 2011, : 180 - 181
  • [3] F508DEL CFTR MODULATORS PARTIALLY RESTORE CHOLESTEROL SIGNALING AND FILLIPIN STAINING IN F508DEL/F508DEL PRIMARY HUMAN AIRWAY EPITHELIAL CELLS
    Kelley, T.
    Corey, D.
    Ostamnn, A.
    Sridharan, A.
    Rezayat, A.
    Sun, H.
    Clancy, J. P.
    PEDIATRIC PULMONOLOGY, 2013, 48 : 222 - 222
  • [4] AVAILABILITY OF F508DEL CFTR FOR SMALL MOLECULE CORRECTION
    Chung, W.
    Goeckeler-Fried, J.
    Brodsky, J.
    Havasi, V
    Rowe, S. M.
    Piazza, G. A.
    Keeton, A. B.
    Sorscher, E. J.
    PEDIATRIC PULMONOLOGY, 2012, 47 : 224 - 224
  • [5] IN UTERO AND POSTNATAL CFTR MODULATOR THERAPY IN F508DEL FERRETS
    Evans, T.
    Liang, B.
    Yan, Z.
    Sun, X.
    Yi, Y.
    Yang, Y.
    Feng, Z.
    Park, S.
    Qi, L.
    Guo, L.
    Engelhardt, J.
    PEDIATRIC PULMONOLOGY, 2020, 55 : S187 - S188
  • [6] Functional analysis of F508del CFTR in native human colon
    van Barneveld, Andrea
    Stanke, Frauke
    Tamm, Stephanie
    Siebert, Benny
    Brandes, Gudrun
    Derichs, Nico
    Ballmann, Manfred
    Junge, Sibylle
    Tuemmler, Burkhard
    BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, 2010, 1802 (11): : 1062 - 1069
  • [7] THE CFTR INTERACTOME: MAKING F508DEL LOOK LIKE WT
    Hutt, D. M.
    Loguercio, S.
    Pankow, S.
    Roth, Martino D.
    Bamberger, C.
    Su, A., I
    Yates, J. R., III
    Balch, W. E.
    PEDIATRIC PULMONOLOGY, 2013, 48 : 211 - 211
  • [8] MOLECULAR CHARACTERIZATION OF F508DEL/F508DEL FERRET MODEL OF CYSTIC FIBROSIS
    Evans, T.
    Sun, X.
    Yan, Z.
    Iiang, B.
    Yi, Y.
    Yang, Y.
    Feng, Z.
    Park, S.
    Qi, L.
    Engelhardt, J.
    PEDIATRIC PULMONOLOGY, 2019, 54 : S323 - S323
  • [9] DETECTION OF CORRECTED F508DEL CFTR IN PATIENTS TREATED WITH IVACAFTOR/LUMACAFTOR
    Ostmann, A. J.
    Ray, K.
    Thornton, K.
    Rowe, S.
    Solomon, G.
    Clancy, J.
    PEDIATRIC PULMONOLOGY, 2015, 50 : 295 - 295
  • [10] KNOCKING DOWN ERDJ4 TO RESCUE F508DEL CFTR
    Huang, Y.
    Arora, K.
    Mun, K.
    Yang, F.
    Yarlagadda, S.
    Weaver, T.
    Naren, A.
    PEDIATRIC PULMONOLOGY, 2018, 53 : 148 - 149
12345