Interferon β-1a in chronic inflammatory demyelinating polyneuropathy -: Case report
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作者:
Villa, AM
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Univ Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, ArgentinaUniv Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, Argentina
Villa, AM
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Garcea, O
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Univ Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, ArgentinaUniv Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, Argentina
Garcea, O
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Di Egidio, M
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Univ Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, ArgentinaUniv Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, Argentina
Di Egidio, M
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Saizar, R
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Univ Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, ArgentinaUniv Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, Argentina
Saizar, R
[1
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Sica, REP
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Univ Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, ArgentinaUniv Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, Argentina
Sica, REP
[1
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机构:
[1] Univ Buenos Aires, Dept Neurol, Hosp Ramos Meja, Div Neurol,Fac Med, RA-1221 Buenos Aires, DF, Argentina
Chronic inflammatory demyelinating polyneuropathy (CIDP) is an acquired immune-mediated neuropathy. It presents with a course of progression which may be slow and steady or step-wise or relapsing. Sensory ataxic polyneuropathy may be the only clinical manifestation of this disease. Treatment with interferon beta 1a (INF beta 1a) has been tried with different results in patients who were refractory to other, more conventional, immunomodulatory therapies. Here we report on a patient who had a relapsing form of pure sensory ataxic CIDP and who failed to respond to intravenous human immunoglobulin. He was put on INF beta 1a for 3 years. During this period he suffered no relapses while his condition stabilized.