ASSESSMENT OF CFTR CU SECRETION IN HUMAN COLON & EFFICACY OF F508DEL-CFTR CORRECTORS IN HUMAN NATIVE TISSUES

被引：0
|
作者：
Sousa, M. [1 ,2 ]
Servidoni, M. D. [3 ]
Vinagre, A. M. [3 ]
Bonadia, L. [3 ]
Cardoso, S. R. [3 ]
Kmit, A. [3 ]
Ramalho, A. S. [1 ,2 ]
Bertuzzo, C. S. [3 ]
Ribeiro, A. F. [3 ]
Kunzelmann, K. [4 ]
Amaral, M. D. [1 ,2 ]
机构：
[1] INSA, DG, Lisbon, Portugal
[2] FCUL, DQB, Lisbon, Portugal
[3] Univ Estadual Campinas, FCM, Campinas, Brazil
[4] UR, IP, Regensburg, Germany
来源：
PEDIATRIC PULMONOLOGY | 2010年
关键词：
CYSTIC-FIBROSIS; RESCUE;
D O I：
暂无
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
引用
收藏
页码：300 / 301
页数：2
相关论文
共 50 条
  • [1] Correctors modify the bicarbonate permeability of F508del-CFTR
    Fiore, Michele
    Picco, Cristiana
    Moran, Oscar
    SCIENTIFIC REPORTS, 2020, 10 (01)
  • [2] Correctors modify the bicarbonate permeability of F508del-CFTR
    Michele Fiore
    Cristiana Picco
    Oscar Moran
    Scientific Reports, 10
  • [3] DISCOVERY AND CHARACTERIZATION OF POTENT F508DEL-CFTR CORRECTORS
    Bandiera, T.
    Sorana, F.
    Berti, F.
    Rodriguez-Gimeno, A.
    Di Fruscia, P.
    Brindani, N.
    Bertozzi, Mandrup S.
    Ottonello, G.
    Armirotti, A.
    Span, R.
    Bertorelli, R.
    Penna, I
    Margaroli, N.
    Russo, D.
    Caci, E.
    Ferrera, L.
    Tomati, V
    Pesce, E.
    Scudieri, P.
    Bertozzi, F.
    Pedemonte, N.
    Galietta, L. J.
    PEDIATRIC PULMONOLOGY, 2017, 52 : S217 - S217
  • [4] Extracellular phosphate enhances the function of F508del-CFTR rescued by CFTR correctors
    Saint-Criq, Vinciane
    Wang, Yiting
    Delpiano, Livia
    Lin, JinHeng
    Sheppard, David N.
    Gray, Michael A.
    JOURNAL OF CYSTIC FIBROSIS, 2021, 20 (05) : 843 - 850
  • [5] Functional analysis of F508del CFTR in native human colon
    van Barneveld, Andrea
    Stanke, Frauke
    Tamm, Stephanie
    Siebert, Benny
    Brandes, Gudrun
    Derichs, Nico
    Ballmann, Manfred
    Junge, Sibylle
    Tuemmler, Burkhard
    BIOCHIMICA ET BIOPHYSICA ACTA-MOLECULAR BASIS OF DISEASE, 2010, 1802 (11): : 1062 - 1069
  • [6] Functional rescue of F508del-CFTR using small molecule correctors
    Molinski, Steven
    Eckford, Paul D. W.
    Pasyk, Stan
    Ahmadi, Saumel
    Chin, Stephanie
    Bear, Christine E.
    FRONTIERS IN PHARMACOLOGY, 2012, 3
  • [7] Identification of novel F508del-CFTR traffic correctors among triazole derivatives
    Bacalhau, Mafalda
    Ferreira, Filipa C.
    Kmit, Arthur
    Souza, Felipe R.
    da Silva, Veronica D.
    Pimentel, Andre S.
    Amaral, Margarida D.
    Buarque, Camilla D.
    Lopes-Pacheco, Miqueias
    EUROPEAN JOURNAL OF PHARMACOLOGY, 2023, 938
  • [8] Small molecule correctors synergistically restore F508del-CFTR function and processing
    Boinot, C.
    Souchet, M. Jollivet
    Clement, R.
    Norez, C.
    Becq, F.
    FUNDAMENTAL & CLINICAL PHARMACOLOGY, 2014, 28 : 74 - 74
  • [9] INHIBITORS OF CFTR UBIQUITINATION ACT SYNERGISTICALLY WITH SMALL MOLECULE CORRECTORS TO ENHANCE F508DEL-CFTR MATURATION AND ACTIVITY
    Goeckeler-Fried, J.
    Chung, W.
    Chiang, A.
    Denny, R. A.
    Weissman, A. M.
    Sorscher, E. J.
    Brodsky, J. L.
    PEDIATRIC PULMONOLOGY, 2015, 50 : 196 - 196
  • [10] Correctors of the basic trafficking defect of the mutant F508del-CFTR that causes cystic fibrosis
    Birault, Veronique
    Solari, Roberto
    Hanrahan, John
    Thomas, David Y.
    CURRENT OPINION IN CHEMICAL BIOLOGY, 2013, 17 (03) : 353 - 360
12345