Valve-sparing aortic root replacement and aortic valve repair for a 2-year-old girl with Loeys-Dietz syndrome

被引：0
|
作者：
Shiraishi, Shuichi [1 ]
Okita, Yutaka [2 ]
Watanabe, Maya [1 ]
Tsuchida, Masanori [1 ]
机构：
[1] Niigata Univ, Div Thorac & Cardiovasc Surg, Grad Sch Med & Dent Sci, Niigata, Japan
[2] Takatsuki Gen Hosp, Dept Cardiovasc Surg, Takatsuki, Osaka, Japan
来源：
INTERACTIVE CARDIOVASCULAR AND THORACIC SURGERY | 2022年 / 34卷 / 06期
关键词：
Loeys-Dietz syndrome; Valve-sparing aortic root replacement; Aortic valve repair; CHILDREN;
D O I：
10.1093/icvts/ivab367
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
We report the case of a 2-year-old girl with Loeys-Dietz syndrome complicated by aortic root dilatation and aortic regurgitation. We performed valve-sparing aortic root replacement with reimplantation technique and aortic valve repair using central plication and free-margin reinforcement simultaneously. The postoperative course was uneventful and the latest echocardiography, 5 years after procedure, revealed trivial aortic insufficiency. Loeys-Dietz syndrome (LDS) is a rare connective tissue disorder characterized by arterial tortuosity and aneurysm, hypertelorism and bifid uvula or cleft palate.
引用
收藏
页码：1174 / 1176
页数：3
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