Hepatic fibrosis with adult polycystic kidney and liver disease.

被引：0
|
作者：
Sanchez, EM [1 ]
Martel, AC [1 ]
Perez, CS [1 ]
Ortega, SS [1 ]
Saade, MEA [1 ]
机构：
[1] HOSP EL SABINAL & NUESTRA SENORA DEL PINO,MED INTERNA SERV,LAS PALMAS,SPAIN
来源：
REVISTA ESPANOLA DE ENFERMEDADES DIGESTIVAS | 1996年 / 88卷 / 02期
关键词：
hepatic fibrosis; polycystic liver disease;
D O I：
暂无
中图分类号：
R57 [消化系及腹部疾病];
学科分类号：
摘要：
Objective: A case of hepatic fibrosis in adult polycystic liver disease is reported. This association, commonly present in infancy, is exceptional in the adult polycystic liver disease. Patient: We report a 69-years-old female with adult polycystic kidney and liver disease with fatal hepatic failure, portal hypertension and renal failure. An autopsy was performed showing hepatic and renal polycystic disease with hepatic fibrosis. Conclusion: Hepatic fibrosis is a rarely associated phenomenon with adult polycystic liver disease. This data may suggest a relation of this entity with infancy fibropolycystic liver disease.
引用
收藏
页码：145 / 149
页数：5
相关论文
共 50 条
  • [1] KIDNEY POLYCYSTIC DISEASE IN ADULT CONGENTIAL HEPATIC-FIBROSIS
    DUPOND, JL
    MIGUET, JP
    CARBILLET, JP
    STHILLIER, Y
    PEROL, C
    LECONTEDESFLORIS, R
    [J]. ANNALS OF INTERNAL MEDICINE, 1978, 88 (04) : 514 - 515
  • [2] Combined liver and kidney transplantation for polycystic kidney and liver disease.
    Francoz, C
    Paradis, V
    Legendre, C
    Sommacale, D
    Sauvanet, A
    Valla, D
    Belghiti, J
    Durand, F
    [J]. LIVER TRANSPLANTATION, 2005, 11 (07) : C57 - C57
  • [3] Results of combined liver/kidney transplantation for polycystic liver and kidney disease.
    Fangmann, Josef
    Bartels, Michael
    Harms, Jens
    Scheler, Joerg
    Hauss, Johann
    [J]. AMERICAN JOURNAL OF TRANSPLANTATION, 2007, 7 : 557 - 557
  • [4] Prospective evaluation of kidney and liver disease in autosomal recessive polycystic kidney disease-congenital hepatic fibrosis
    Majeed, Nehna Abdul
    Font-Montgomery, Esperanza
    Lukose, Linda
    Bryant, Joy
    Veppumthara, Peter
    Choyke, Peter L.
    Turkbey, Ismail B.
    Heller, Theo
    Gahl, William A.
    Gunay-Aygun, Meral
    [J]. MOLECULAR GENETICS AND METABOLISM, 2020, 131 (1-2) : 267 - 276
  • [5] Hepatic fibrogenesis in cystic fibrosis liver disease.
    Lewindon, PJ
    Pereira, TN
    Blanch, NL
    Murphy, TL
    Greco, SA
    Bridle, KR
    Smith, JL
    Walker, NI
    Shepherd, RW
    Ramm, GA
    [J]. HEPATOLOGY, 1999, 30 (04) : 501A - 501A
  • [6] A 13 year experience with polycystic liver disease in a population of patients with polycystic kidney disease.
    Ortega, SJ
    Peltekian, K
    Walsh, MJ
    [J]. AMERICAN JOURNAL OF TRANSPLANTATION, 2005, 5 : 334 - 334
  • [7] Congenital Hepatic Fibrosis and Autosomal Recessive Polycystic Kidney Disease
    Srinath, Arvind
    Shneider, Benjamin L.
    [J]. JOURNAL OF PEDIATRIC GASTROENTEROLOGY AND NUTRITION, 2012, 54 (05): : 580 - 587
  • [8] Studies on the reversibility of hepatic fibrosis in alcoholic liver disease.
    Tsutsumi, M
    Urashima, S
    Ueshima, Y
    Kawahara, H
    Takase, S
    [J]. HEPATOLOGY, 1996, 24 (04) : 1860 - 1860
  • [9] Congenital Hepatic Fibrosis in Autosomal Recessive Polycystic Kidney Disease
    Wen, Jessica
    [J]. CTS-CLINICAL AND TRANSLATIONAL SCIENCE, 2011, 4 (06): : 460 - 465
  • [10] Congenital Hepatic Fibrosis in Autosomal Recessive Polycystic Kidney Disease
    Gunay-Gun, M.
    Font-Montgomery, E.
    Lukose, L.
    [J]. PRACTICAL GASTROENTEROLOGY, 2013, 37 (04) : 54 - 54
12345