Sinonasal Manifestations of Severe Cherubism: A Case with 11-year Follow-up

被引:1
|
作者
Jung, Keun-Woo [1 ]
Yun, Ji Min [1 ]
Lee, Jeon Mi [1 ]
Choi, Ick Soo [1 ,2 ]
机构
[1] Inje Univ, Ilsan Paik Hosp, Dept Otorhinolaryngol Head & Neck Surg, Coll Med, Goyang, South Korea
[2] Inje Univ, Ilsan Paik Hosp, Dept Otorhinolaryngol Head & Neck Surg, Coll Med, 170 Juhwa Ro,Ilsanseo Gu, Goyang 10380, Gyeonggi, South Korea
基金
新加坡国家研究基金会;
关键词
cherubism; craniofacial abnormalities; maxillofacial abnormalities; genetic disease; inborn; pediatrics; paranasal sinus; nasal cavity;
D O I
10.1177/01455613221127588
中图分类号
R76 [耳鼻咽喉科学];
学科分类号
100213 ;
摘要
Cherubism, a type of fibroosteodysplasia, is a rare hereditary disease that causes variable degrees of facial deformity in children. Hypertrophy of the mandible is the most common symptom, but in severe cases, the disease affects the eyes, teeth, and sinonasal cavity. There have been few reports regarding sinonasal complications and no standard treatment has been established. This paper reports long-term treatment of severe cherubism that invaded the sinonasal cavity treated with consecutive endoscopic sinonasal surgeries.
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页数:6
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