Deficiency of mannan-binding lectin - a risk factor for severe disease in cystic fibrosis?

被引:0
|
作者
Carlsson, M
Sjholm, AG
Eriksson, L
Kornflt, R
Mared, L
Meyer, P
Segelmark, M
Truedsson, L
机构
[1] Lund Univ, Inst Lab Med, Sect Microbiol Immunol & Glycobiol, Malmo, Sweden
[2] Lund Univ, Dept Resp Med, Malmo, Sweden
[3] Lund Univ, Dept Pediat, Malmo, Sweden
[4] Lund Univ, Dept Nephrol, Malmo, Sweden
关键词
MBL; cystic fibrosis;
D O I
暂无
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:207 / 208
页数:2
相关论文
共 50 条
  • [1] MANNAN-BINDING LECTIN DEFICIENCY IN A CHILD: IS IT A THING OR NOT?
    Pitso, Boitumelo
    Pillay, Chantal
    de Waal, Pieter
    CURRENT ALLERGY & CLINICAL IMMUNOLOGY, 2023, 36 (03) : 166 - 171
  • [2] Clinical manifestations of mannan-binding lectin deficiency
    Thiel, S
    Frederiksen, PD
    Jensenius, JC
    MOLECULAR IMMUNOLOGY, 2006, 43 (1-2) : 86 - 96
  • [3] Mannan-Binding Lectin in Cardiovascular Disease
    Pdgowska-Klimek, Izabela
    Cedzynski, Andmaciej
    BIOMED RESEARCH INTERNATIONAL, 2014, 2014
  • [4] Mannan-binding lectin deficiency in pediatric patients with inflammatory bowel disease
    Bak-Romaniszyn, Leokadia
    Szala, Agnieszka
    Sokolowska, Anna
    Mierzwa, Grazyna
    Czerwionka-Szaflarska, Mieczyslawa
    Swierzko, Anna St.
    Zeman, Krzysztof
    Cedzynski, Maciej
    SCANDINAVIAN JOURNAL OF GASTROENTEROLOGY, 2011, 46 (10) : 1275 - 1278
  • [5] Deficiency of the mannan-binding lectin pathway of complement and poor outcome in cystic fibrosis:: bacterial colonization may be decisive for a relationship
    Carlsson, M
    Sjöholm, AG
    Eriksson, L
    Thiel, S
    Jensenius, JC
    Segelmark, M
    Truedsson, L
    CLINICAL AND EXPERIMENTAL IMMUNOLOGY, 2005, 139 (02): : 306 - 313
  • [6] The mannan-binding lectin pathway and lung disease in cystic fibrosis-dysfunction of mannan-binding lectin-associated serine protease 2 (MASP-2) may be a major modifier
    Olesen, H. V.
    Jensenius, J. C.
    Steffensen, R.
    Thiel, S.
    Schiotz, P. O.
    CLINICAL IMMUNOLOGY, 2006, 121 (03) : 324 - 331
  • [7] Susceptibility to severe infections in a family due to inherited deficiency of mannan-binding lectin.
    Martin, P
    Good, RA
    Haraguchi, S
    Johnson, L
    Day, NK
    CLINICAL IMMUNOLOGY, 2002, 103 (03) : S127 - S128
  • [8] Mannan-binding lectin in malignancy
    Swierzko, Anna S.
    Kilpatrick, David C.
    Cedzynski, Maciej
    MOLECULAR IMMUNOLOGY, 2013, 55 (01) : 16 - 21
  • [9] Mannan-binding lectin in neonates
    Szala, A.
    MacDonald, S.
    Domzalska-Popadiuk, I.
    Atkinson, A.
    Cedzynski, M.
    Swierzko, A.
    Szemraj, J.
    Borkowska, M.
    Szczapa, J.
    Matsushita, M.
    Turner, M.
    Kilpatrick, D.
    INTERNATIONAL JOURNAL OF ANTIMICROBIAL AGENTS, 2007, 29 : S497 - S498
  • [10] Quantification of mannan-binding lectin
    Frederiksen, Pernille D.
    Thiel, Steffen
    Jensen, Lisbeth
    Hansen, Annette G.
    Matthiesen, Finn
    Jensenius, Jens Chr.
    JOURNAL OF IMMUNOLOGICAL METHODS, 2006, 315 (1-2) : 49 - 60