Embryonal Rhabdomyosarcoma of Testis

被引:0
|
作者
Bhatia, Gunjan [1 ]
Goyal, Namita [1 ]
机构
[1] RNT Med Coll, Dept Pathol, Udaipur, Rajasthan, India
关键词
Aggressive tumour; Inguinal orchidectomy; Para testicular tissue; ADULT;
D O I
10.7860/JCDR/2019/42331.13254
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Embroynal Rhabdomyosarcoma of the testis is a rare and aggressive tumour, mostly seen in children and young adults. It usually originates from the para testicular tissue. Intra testicular rhabdomyosarcoma of testis is a rare entity. The authors present a case of testicular rhabdomyosarcoma in a 28-year-old male patient. The patient presented to the surgical OPD with a painless scrotal mass of two months duration. A clinical diagnosis of testicular mass was made and patient was investigated and treated accordingly. Ultrasound (USG) revealed a right sided testicular mass measuring 16x6 cm. Patient underwent right sided inguinal orchidectomy. On microscopic examination tumour had varying degrees of cellularity, alternating densely packed hypercellular areas of oval to spindle shaped cells showing vesicular nucleus and pleomorphism along with loosely textured myxoid areas in between. IHC for keratin, Alpha-Fetoprotein (AFP), Inhibin and CD 117 were negative while Immunohistochemistry (IHC) for myogenin was positive. On basis of histopathology and IHC a final diagnosis of Embryonal Rhabdomyosarcoma was given. Intra testicular rhabdomyosarcoma of the testis is a rare tumour but should be kept in mind when dealing with a case of scrotal mass. Rarity of this entity makes it a strong learning point for our fellow clinicians and pathologists.
引用
收藏
页码:ED01 / ED03
页数:3
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