Supravalvular aortic stenosis, pulmonary artery stenosis, and coronary artery stenosis in twins

被引:6
|
作者
Nakanishi, T [1 ]
Iwasaki, Y [1 ]
Momma, K [1 ]
Imai, Y [1 ]
机构
[1] SHINSHU UNIV, SCH MED, DEPT PEDIAT, MATSUMOTO, NAGANO 390, JAPAN
关键词
supravalvular aortic stenosis; pulmonary arterial stenosis; coronary ostial stenosis; twins;
D O I
10.1007/s002469900028
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Supravalvular aortic stenosis (SVAS) is rare in twins, We report monozygotic twins, both of whom had SVAS, coronary ostial stenosis, and peripheral pulmonary arterial stenosis, but no other phenotypic features of Williams syndrome. One of the twins died suddenly, but the SVAS and the right and left coronary ostial stenoses were enlarged successfully at operation in the other twin.
引用
收藏
页码:125 / 128
页数:4
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